Congenital coagulopathies

Syn .: Congenital blood coagulation disorders.

Def .: Congenital hemorrhagic diathesis caused by deficiencies or disturbances in the function of a single blood coagulation factor. These diseases include: haemophilia A, haemophilia B, and von Willebrand disease.

Klin.: Hemophilia.

Lit.: [1] Journeycake J.M., Buchanan G.R.: Coagulation disorders. Pediatr Rev 2003, 24; 83-91. [2] Blanchette V.S., Sparling C., Turner C.: Inherited bleeding disorders. Baillieres Clin Haematol 1991, 4; 291-332.

Source: A. Kaszuba, Z. Adamski: “Lexicon of dermatology”; XNUMXst edition, Czelej Publishing House

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